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EntityQ1153641· pop 17· linked from 60 articles

Wolfram syndrome

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Also known as DIDMOAD, Diabetes mellitus AND insipidus with optic atrophy AND deafness (disorder), WFS, Diabetes mellitus AND insipidus with optic atrophy AND deafness, Diabetes Insipidus, Diabetes Mellitus, Optic Atrophy, and Deafness Syndrome, DIDMOAD syndrome, Diabetes insipidus-diabetes mellitus-optic atrophy-deafness syndrome, Diabetes insipidus-diabetes mellitus-optic atrophy-hearing loss syndrome

rare disease in which a human simultaneously has diabetes insipidus, diabetes, optic nerve atrophy and deafness syndrome

Research

1,052 papers

via PubMed

Wikidata facts

Image
Photographic image of the patient right eye showing optic atrophy without diabetic retinopathy Wolfram syndrome.jpg
Show 12 more facts
afflicts
Homo sapiens
has cause
mutation
Commons category
Wolfram syndrome
NCI Thesaurus ID
C35133
health specialty
endocrinology
ICD-9-CM
250.90
has phenotype
diabetes insipidus
external data available at URL
www.nanbyou.or.jp/entry/4789
genetic association
WFS1
on focus list of Wikimedia project
WikiProject Medicine
short name
Wolfram-Syndrom
Sources (7)

via Wikidata · CC0