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EntityQ779203· pop 6· linked from 19 articles

CINCA syndrome

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Also known as NOMID syndrome, chronic infantile neurological cutaneous articular syndrome, Prieur-Griscelli syndrome, infantile-onset multisystem inflammatory disease, cryopyrin-associated periodic syndrome 3, IOMID syndrome, chronic neurologic cutaneous and articular syndrome, neonatal-onset multisystem inflammatory disease

Chronic Infantile Neurological, Cutaneous, and Articular (CINCA) syndrome is characterised by skin rash, joint involvement, chronic meningitis with granulocytes and, in some cases, sensorineural hearing loss and ocular signs

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health specialty
rheumatology
NCI Thesaurus ID
C116380
ICD-9-CM
759.89
genetic association
NLRP3
on focus list of Wikimedia project
WikiProject Medicine
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