CINCA syndrome
Sign in to saveAlso known as NOMID syndrome, chronic infantile neurological cutaneous articular syndrome, Prieur-Griscelli syndrome, infantile-onset multisystem inflammatory disease, cryopyrin-associated periodic syndrome 3, IOMID syndrome, chronic neurologic cutaneous and articular syndrome, neonatal-onset multisystem inflammatory disease
Chronic Infantile Neurological, Cutaneous, and Articular (CINCA) syndrome is characterised by skin rash, joint involvement, chronic meningitis with granulocytes and, in some cases, sensorineural hearing loss and ocular signs
Wikidata facts
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- health specialty
- rheumatology
- exact match
- www.orpha.net/ORDO/Orphanet_1451
- NCI Thesaurus ID
- C116380
- ICD-9-CM
- 759.89
- genetic association
- NLRP3
- on focus list of Wikimedia project
- WikiProject Medicine
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