Skip to content
GeneQ18027320· pop 7· linked from 24 articles

Also known as DBP, MFE-2, MPF-2, PRLTS1, SDR8C1, hydroxysteroid (17-beta) dehydrogenase 4, hydroxysteroid 17-beta dehydrogenase 4

D-bifunctional protein (DBP), also known as peroxisomal multifunctional enzyme type 2 (MFP-2), as well as 17β-hydroxysteroid dehydrogenase type IV (17β-HSD type IV) is a protein that in humans is encoded by the HSD17B4 gene. It's an alcohol oxidoreductase, specifically 17β-Hydroxysteroid dehydrogenase. It is involved in fatty acid β-oxidation and steroid metabolism (cf. steroidogenesis).

Gene data

HSD17B4
Name
hydroxysteroid 17-beta dehydrogenase 4
Type
protein-coding
Aliases
DBP, MFE-2, MFP-2, MPF-2, PRLTS1, SDR8C1

The protein encoded by this gene is a bifunctional enzyme that is involved in the peroxisomal beta-oxidation pathway for fatty acids. It also acts as a catalyst for the formation of 3-ketoacyl-CoA intermediates from both straight-chain and 2-methyl-branched-chain fatty acids. Defects in this gene that affect the peroxisomal fatty acid beta-oxidation activity are a cause of D-bifunctional protein deficiency (DBPD). An apparent pseudogene of this gene is present on chromosome 8. Multiple alternatively spliced transcript variants encoding distinct isoforms have been found for this gene. [provided by RefSeq, May 2014].

via MyGene.info

Wikidata facts

Image
Protein HSD17B4 PDB 1ikt.png
Show 6 more facts
HomoloGene ID
358
genomic start
119452473
genomic end
118972894
cytogenetic location
5q23.1
Commons category
HSD17B4
Sources (4)

via Wikidata · CC0

~2 min read

Article

4 sections
Contents
  • Function
  • See also
  • References
  • Further reading

D-bifunctional protein (DBP), also known as peroxisomal multifunctional enzyme type 2 (MFP-2), as well as 17β-hydroxysteroid dehydrogenase type IV (17β-HSD type IV) is a protein that in humans is encoded by the HSD17B4 gene. It's an alcohol oxidoreductase, specifically 17β-Hydroxysteroid dehydrogenase. It is involved in fatty acid β-oxidation and steroid metabolism (cf. steroidogenesis).

== Function ==

Available in 6 languages

via Wikidata sitelinks · CC0

Connections

Categories