EntityQ1617658· pop 8· linked from 69 articleshyper IgM syndromeSign in to saveprimary immune deficiency disorders characterized by defective CD40 signalingConnectionsB-cellEntityCD40LGGenemedicineEntityHIV/AIDSEntityphysicianEntityInternational Standard Book NumberEntitydiarrheaEntityallergyEntitysurgeryEntitypsychiatryEntitypathologyEntitydigital object identifierEntityinfectionEntityInternational Standard Serial NumberEntitycardiologyEntityneurologyEntitygynaecologyEntityophthalmologyEntityoncologyEntitymagnetic resonance imagingEntityCategoriesCommons link is the pagenamePredominantly antibody deficienciesRare syndromesSyndromes affecting immunity