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EntityQ3913024· pop 7· linked from 43 articles

リンパ管肉腫

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Also known as Lymphangiosarcoma of Stewart and Treves, Stewart-Treves syndrome (disorder), malignant Lymphangioendothelioma, skin lymphangiosarcoma, Stewart-Treves syndrome, Lymphangiosarcoma of the Skin, Lymphangiosarcoma of Skin

Lymphangiosarcoma is a rare cancer which occurs in long-standing cases of primary or secondary lymphedema (swelling due to lymphatic system obstruction). It involves either the upper or lower lymphedematous extremities but is most common in upper extremities. Although its name implies lymphatic origin, it is believed to arise from endothelial cells and may be more accurately referred to as angiosarcoma.

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Wikidata facts

Subclass of
disease
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NCI Thesaurus ID
C4490
ICD-9-CM
171.2
health specialty
oncology
on focus list of Wikimedia project
WikiProject Medicine
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Article · 日本語

リンパ管肉腫(Lymphangiosarcoma)は、原発性または続発性のリンパ浮腫を長年患っている場合に発生する稀な悪性腫瘍である。上肢または下肢のリンパ浮腫に発生するが、上肢に多く見られる。名前からはリンパ由来と思われるが、内皮細胞から発生すると考えられており、より正確には脈管肉腫と呼ばれる事がある。

Abstract from DBpedia / Wikipedia · CC BY-SA

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