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EntityQ3913024· pop 7· linked from 43 articles

linfangiossarcoma

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Also known as Lymphangiosarcoma of Stewart and Treves, Stewart-Treves syndrome (disorder), malignant Lymphangioendothelioma, skin lymphangiosarcoma, Stewart-Treves syndrome, Lymphangiosarcoma of the Skin, Lymphangiosarcoma of Skin

Lymphangiosarcoma is a rare cancer which occurs in long-standing cases of primary or secondary lymphedema (swelling due to lymphatic system obstruction). It involves either the upper or lower lymphedematous extremities but is most common in upper extremities. Although its name implies lymphatic origin, it is believed to arise from endothelial cells and may be more accurately referred to as angiosarcoma.

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Wikidata facts

Subclass of
disease
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NCI Thesaurus ID
C4490
ICD-9-CM
171.2
health specialty
oncology
on focus list of Wikimedia project
WikiProject Medicine
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Article · Português

Linfangiossarcoma é um tumor maligno raro, que ocorre em casos de linfedema crônico primário ou secundário . Pode envolver qualquer uma das extremidades, mas é mais comum em membros superiores. Apesar de seu nome implicar uma origem linfática, acredita-se que surja a partir de células endoteliais e pode ser mais precisamente denominado como angiossarcoma.

Abstract from DBpedia / Wikipedia · CC BY-SA

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