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DiseaseQ1410851· pop 12· linked from 177 articles

fibromatosis

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The term fibromatosis refers to a group of soft tissue tumors which have certain characteristics in common, including absence of cytologic and clinical malignant features, a histology consistent with proliferation of well-differentiated fibroblasts, an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence. It is classed by the World Health Organization as an intermediate soft tissue tumor related to the sarcoma family. Arthur Purdy Stout coined the term fibromatosis (in the name congenital generalized fibromatosis, describing myofibromatosis), in 1954.

Key facts

Medical condition (new).name
Fibromatosis
Medical condition (new).image
File:Desmoid-type fibromatosis.gross pathology.jpg
Medical condition (new).field
oncology

via Wikipedia infobox

Health references

ICD-10
M72.9 — Fibroblastic disorder, unspecified
Source: U.S. National Library of Medicine (ICD-10-CM · MedlinePlus). Not medical advice.

Clinical Trials

68 registered

via ClinicalTrials.gov

Wikidata facts

Instance of
rare disease
Image
Desmoid-type fibromatosis.gross pathology.jpg
Show 3 more facts
Commons category
Fibromatosis
health specialty
rheumatology
NCI Thesaurus ID
C3042
Sources (3)

via Wikidata · CC0

~3 min read

Encyclopedic overview

9 sections
Contents
  • Diagnosis
  • Juvenile subtypes
  • Adult subtypes
  • Superficial
  • Deep
  • Treatment
  • Terminology
  • References
  • External links

The term fibromatosis refers to a group of soft tissue tumors which have certain characteristics in common, including absence of cytologic and clinical malignant features, a histology consistent with proliferation of well-differentiated fibroblasts, an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence. It is classed by the World Health Organization as an intermediate soft tissue tumor related to the sarcoma family. Arthur Purdy Stout coined the term fibromatosis (in the name congenital generalized fibromatosis, describing myofibromatosis), in 1954.

==Diagnosis== ===Juvenile subtypes=== Subtypes of juvenile fibromatosis include: Infantile myofibromatosis: solitary tumors commonly occurring in the head and neck regions; multiple tumors occurring in the skin, subcutaneous tissue, muscles, and/or less commonly bones; or, rarely, tumors occurring in an internal organ(s). Aponeurotic fibroma Infantile digital fibromatosis Aggressive infantile fibromatosis Fibromatosis colli: benign sternocleidomastoid muscle tumor developing in infants within 8 weeks (average: 24 days) of delivery. It generally does not require resection and responds well to physiotherapy. Dermatofibrosis lenticularis (Buschke–Ollendorff syndrome) Fibromatosis hyalinica multiplex (juvenile hyaline fibromatosis) Lipofibromatosis

Excerpted from Wikipedia’s “fibromatosis” article, available under the CC BY-SA 4.0 licence.