🌐EnglishEnglishItalianoفارسی日本語EntityQ87269741· pop 10· linked from 250 articlesisovaleryl-CoA dehydrogenaseclass of enzymesResearch277 papersPractical Considerations for the Diagnosis and Management of Isovaleryl-CoA-Dehydrogenase Deficiency (Isovaleric Acidemia): Systematic Search and Review and Expert Opinions.International journal of neonatal screening · 2025Kinetic and spectral properties of isovaleryl-CoA dehydrogenase and interaction with ligands.Biochimie · 2015Classic Isovaleric Acidemia.1993Three linked variants have opposing regulatory effects on isovaleryl-CoA dehydrogenase gene expression.Human molecular genetics · 2024Isovaleryl-CoA dehydrogenase activity in isovaleric acidemia fibroblasts using an improved tritium release assay.Pediatric research · 1986via PubMedAvailable in 10 languages日本語ItalianoBosnianSerbianSerbian (Latin)SlovakTatarUkrainianفارسیvia Wikidata sitelinks · CC0ConnectionsenzymeEntityQ180686EntityCategoriesEC 1.3.8Enzymes of known structureFlavoproteinsMitochondrial proteins