🌐EnglishEnglishDeutschEspañolFrançaisItalianoPolskiSvenskaالعربية日本語EntityQ1337441· pop 9· linked from 48 articlesKostmann syndromegroup of diseases that affect myelopoiesis, causing a congenital form of neutropeniaResearch337 papersKostmann syndrome and severe congenital neutropenia.Seminars in hematology · 2002[Kostmann syndrome].Ryoikibetsu shokogun shirizu · 1998Kostmann syndrome or infantile genetic agranulocytosis, part two: Understanding the underlying genetic defects in severe congenital neutropenia.Acta paediatrica (Oslo, Norway : 1992) · 2007Kostmann Syndrome With Neurological Abnormalities: A Case Report and Literature Review.Frontiers in pediatrics · 2020Oral microbial dysbiosis in patients with Kostmann syndrome.Journal of medical microbiology · 2019via PubMedConnectionsdominanceEntityacute myeloid leukemiaEntityCategoriesAutosomal dominant disordersAutosomal recessive disordersCongenital defects of phagocyte number, function, or bothEnzyme defectsRare diseasesSyndromes affecting blood