Skip to content
GeneQ18030978· pop 5· linked from 76 articles

Also known as ARCL2B, ARCL3B, P5C, P5CR, PIG45, PP222, PRO3, PYCR

Pyrroline-5-carboxylate reductase 1, mitochondrial is an enzyme that in humans is encoded by the PYCR1 gene.

Gene data

PYCR1
Name
pyrroline-5-carboxylate reductase 1
Type
protein-coding
Aliases
ARCL2B, ARCL3B, P5C, P5CR, PIG45, PP222, PRO3, PYCR

This gene encodes an enzyme that catalyzes the NAD(P)H-dependent conversion of pyrroline-5-carboxylate to proline. This enzyme may also play a physiologic role in the generation of NADP(+) in some cell types. The protein forms a homopolymer and localizes to the mitochondrion. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2013].

via MyGene.info

Gene · Ensembl

pyrroline-5-carboxylate reductase 1

Symbol
PYCR1
Biotype
Protein coding
Organism
Homo sapiens
Location
17:81,932,378-81,942,412
Strand
Reverse (−)
Assembly
GRCh38
View on Ensembl →

via Ensembl · EMBL-EBI

Wikidata facts

Image
Protein PYCR1 PDB 2ger.png
Show 5 more facts
HomoloGene ID
56002
genomic end
79900288
genomic start
79890260
cytogenetic location
17q25.3
Sources (4)

via Wikidata · CC0

~1 min read

Article

3 sections
Contents
  • References
  • Further reading
  • External links

Pyrroline-5-carboxylate reductase 1, mitochondrial is an enzyme that in humans is encoded by the PYCR1 gene.

This gene encodes an enzyme that catalyzes the NAD(P)H-dependent conversion of pyrroline-5-carboxylate to proline. This enzyme may also play a physiologic role in the generation of NADP(+) in some cell types. The protein forms a homopolymer and localizes to the mitochondrion. Alternate splicing results in two transcript variants encoding different isoforms. As reported by Bruno Reversade and colleagues, PYCR1 deficiency in humans causes a progeroid disease known as De Barsy Syndrome mainly affecting connective tissues with dermis thinning and bone fragility.

Available in 5 languages

via Wikidata sitelinks · CC0

Connections

Categories