EntityQ7250337· pop 14· linked from 121 articlespropionic acidemiaSign in to saveorganic acidemia that involes a nonfunctional propionyl CoA carboxylase affecting conversion of aminio acids and fats into sugar for energyConnectionsketoneEntityacidosisEntitycarnitineEntityurea cycleEntitybranched-chain amino acidEntitydominanceEntitypropionyl-CoA carboxylaseEntityUnited StatesCountrySaudi ArabiaCountrybloodEntityMarylandEntitymuscleEntityBaltimoreEntityenzymeEntityinfantEntitygeneEntityWayback MachineEntityamino acidEntityammoniaEntityvomitingEntityCategoriesAmino acid metabolism disordersAutosomal recessive disordersFatty-acid metabolism disordersMitochondrial diseasesRare diseases