هیپرآمونمی
Sign in to saveHyperammonemia, or high ammonia levels, is a metabolic disturbance characterised by an excess of ammonia in the blood. Severe hyperammonemia is a dangerous condition that may lead to brain injury and death. It may be primary or secondary.
Key facts
- Medical condition (new).name
- Hyperammonemia
- Medical condition (new).synonyms
- Hyperammonaemia; High ammonia levels
- Medical condition (new).image
- Ammonia lone electron pair.svg
- Medical condition (new).caption
- Ammonia
- Medical condition (new).causes
- Due to accumulation of argininosuccinate, citrulline, and arginine in the liver when the urea cycle is deficient.
via Wikipedia infobox
Research
5,830 papers- Hyperammonemia in Inherited Metabolic Diseases.Cellular and molecular neurobiology · 2022
- Hyperammonemia syndrome in immunosuppressed individuals.Current opinion in infectious diseases · 2022
- Asparaginase-associated hyperammonemia.Haematologica · 2025
- Inborn Errors of Metabolism with Hyperammonemia: Urea Cycle Defects and Related Disorders.Pediatric clinics of North America · 2018
- Hyperammonemia in urea cycle disorders: A toxic metabolite for the brain.Pediatrics international : official journal of the Japan Pediatric Society · 2025
via PubMed
Wikidata facts
- Instance of
- metabolic disease
Show 8 more facts
- possible treatment
- β-lactulose
- has effect
- neurotoxicity
- health specialty
- endocrinology
- exact match
- purl.obolibrary.org/obo/HP_0001987
- Commons category
- Hyperammonemia
- described by source
- Brockhaus and Efron Encyclopedic Dictionary
- NCI Thesaurus ID
- C98950
- has cause
- sulfadiazine
via Wikidata · CC0