- Other names
- Ayerza syndrome
- Specialty
- Pulmonology , cardiology
- Symptoms
- Chest pain, fatigue
- Usual onset
- 20 to 60 years old
- Duration
- Long term
- Causes
- Unknown
- Risk factors
- Family history, pulmonary embolism , HIV/AIDS , sickle cell disease , cocaine use, COPD , sleep apnea , living at high altitudes
- Diagnostic method
- Following ruling out other potential causes
- Treatment
- Supportive care , various medications, lung transplantation
- Medication
- Epoprostenol , treprostinil , iloprost , bosentan , ambrisentan , macitentan , sildenafil
- Frequency
- 1,000 new cases a year (US)