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GeneQ18030620· pop 6· linked from 10 articles

Also known as HNPCC3, PMSL1, hPMS1, MLH2, PMS1 homolog 1, mismatch repair system component

PMS1 protein homolog 1 is a protein that in humans is encoded by the PMS1 gene.

Gene data

PMS1
Name
PMS1 homolog 1, mismatch repair system component
Type
protein-coding
Position
189,784,085–189,878,385 (+)
Aliases
HNPCC3, MLH2, PMSL1, hPMS1
RefSeq RNA
NM_000534.5, NM_001128143.2, NM_001128144.2, NM_001289408.2, NM_001289409.2
RefSeq protein
NP_000525.1, NP_001121615.1, NP_001121616.1, NP_001276337.1, NP_001276338.1

This gene encodes a protein belonging to the DNA mismatch repair mutL/hexB family. This protein is thought to be involved in the repair of DNA mismatches, and it can form heterodimers with MLH1, a known DNA mismatch repair protein. Mutations in this gene cause hereditary nonpolyposis colorectal cancer type 3 (HNPCC3) either alone or in combination with mutations in other genes involved in the HNPCC phenotype, which is also known as Lynch syndrome. [provided by RefSeq, Jul 2008].

via MyGene.info

Wikidata facts

Image
Protein PMS1 PDB 2cs1.png
Show 5 more facts
HomoloGene ID
449
genomic end
190742355
genomic start
190649107
cytogenetic location
2q32.2
Sources (4)

via Wikidata · CC0

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Article

4 sections
Contents
  • Function
  • Yeast studies
  • References
  • Further reading

PMS1 protein homolog 1 is a protein that in humans is encoded by the PMS1 gene.

== Function ==

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