
Also known as Lymphangiomyomatosis, Lymphangiomyomatosis (morphologic abnormality), lung lymphangioleiomyomatosis, pulmonary lymphangioleiomyomatosis (disorder), pulmonary lymphangioleiomyomatosis, Lymphangioleiomyomatosis; LAM, Lung Lymphangiomyomatosis, Lymphangioleiomyomatosis
Lymphangioleiomyomatosis (LAM) is a rare, progressive and systemic disease that typically results in cystic lung destruction. It predominantly affects women, especially during childbearing years. The term sporadic LAM is used for patients with LAM not associated with tuberous sclerosis complex (TSC), while TSC-LAM refers to LAM that is associated with TSC.
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リンパ脈管筋腫症(リンパみゃっかんきんしゅしょう、英: Lymphangioleiomyomatosis; LAM)とは、主に30歳前後の妊娠可能な年齢の女性に発症し、LAM細胞が肺や縦隔のリンパ節で増殖し病変を形成する疾患。厚生労働省の特定疾患。
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Discovered by embedding cosine similarity (sentence-transformers MiniLM, 384-dim).