
Also known as Lymphangiomyomatosis, Lymphangiomyomatosis (morphologic abnormality), lung lymphangioleiomyomatosis, pulmonary lymphangioleiomyomatosis (disorder), pulmonary lymphangioleiomyomatosis, Lymphangioleiomyomatosis; LAM, Lung Lymphangiomyomatosis, Lymphangioleiomyomatosis
Lymphangioleiomyomatosis (LAM) is a rare, progressive and systemic disease that typically results in cystic lung destruction. It predominantly affects women, especially during childbearing years. The term sporadic LAM is used for patients with LAM not associated with tuberous sclerosis complex (TSC), while TSC-LAM refers to LAM that is associated with TSC.
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A linfangioleimiomatose (LAM) é uma rara doença intersticial pulmonar idiopática que afeta exclusivamente mulheres, tipicamente durante seus anos reprodutivos, caracterizada pela proliferação anormal de células de músculo liso nos pulmões e nos linfáticos retroperitoneais e torácicos.
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Discovered by embedding cosine similarity (sentence-transformers MiniLM, 384-dim).