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GeneQ18030048· pop 5· linked from 327 articles

Also known as NANH, NEU, SIAL1, neuraminidase 1 (lysosomal sialidase), neuraminidase 1

Sialidase-1, is a mammalian lysosomal neuraminidase enzyme which in humans is encoded by the NEU1 gene.

Gene data

NEU1
Name
neuraminidase 1
Type
protein-coding
Aliases
NANH, NEU, SIAL1

The protein encoded by this gene is a lysosomal enzyme that cleaves terminal sialic acid residues from substrates such as glycoproteins and glycolipids. In the lysosome, this enzyme is part of a heterotrimeric complex together with beta-galactosidase and cathepsin A (the latter is also referred to as 'protective protein'). Mutations in this gene can lead to sialidosis, a lysosomal storage disease that can be type 1 (cherry red spot-myoclonus syndrome or normosomatic type), which is late-onset, or type 2 (the dysmorphic type), which occurs at an earlier age with increased severity. [provided by RefSeq, Jul 2008].

via MyGene.info

Gene · Ensembl

neuraminidase 1

Symbol
NEU1
Biotype
Protein coding
Organism
Homo sapiens
Location
Chr HSCHR6_MHC_MCF_CTG1:3,199,729-3,204,976
Strand
Reverse (−)
Assembly
GRCh38
View on Ensembl →

via Ensembl · EMBL-EBI

Wikidata facts

Image
C1-inhibitor.png
Show 5 more facts
HomoloGene ID
375
genomic start
31825436
genomic end
31862905
cytogenetic location
6p21.33
Sources (5)

via Wikidata · CC0

~1 min read

Article

5 sections
Contents
  • Function
  • Clinical significance
  • Interactions
  • References
  • Further reading

Sialidase-1, is a mammalian lysosomal neuraminidase enzyme which in humans is encoded by the NEU1 gene.

== Function ==

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via Wikidata sitelinks · CC0

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